vspВопросы современной педиатрииCurrent Pediatrics1682-55271682-5535Издательство «ПедиатрЪ»10.15690/vsp.v20i1.2240vsp-2562Research ArticleКЛИНИЧЕСКОЕ НАБЛЮДЕНИЕCLINICAL OBSERVATIONSKID-синдром, осложненный множественными абсцессами кожи теменной области: клинический случайKID Syndrome Complicated by Multiple Abscesses of the Parietal Region Skin: Clinical Casehttps://orcid.org/0000-0002-8390-822XБебенинаА. А.BebeninaAnastasia A.

Бебенина Анастасия Александровна - ординатор 2-го года обучения кафедры детской хирургии педиатрического факультета РНИМУ им. Н.И. Пирогова.117997, Москва, ул. Островитянова, д. 1.

 

anastasia.bebenina@yandex.ruhttps://orcid.org/0000-0001-5562-8397ЧундоковаМ. А.ChundokovaMadina A.СмирновА. Н.SmirnovAlexey N.https://orcid.org/0000-0002-5512-9894ГолованёвМ. А.GolovanevMaxim A.

117997, Москва, ул. Островитянова, д. 1.

https://orcid.org/0000-0002-4424-0271ДокшукинаА. А.DokshukinaAlina A.Российский национальный исследовательский медицинский университет им. Н.И. ПироговаРоссияPirogov Russian National Research Medical UniversityRussian FederationДетская городская клиническая больница им. Н.Ф. ФилатоваРоссияChildren’s City Clinical Hospital named after N.F. FilatovRussian FederationНаучный медицинский исследовательский центр акушерства, гинекологии и перинатологии им. акад. В.И. КулаковаРоссияNational Medical Research Center for Obstetrics, Gynecology and Perinatology n.a. Academician V.I. KulakovRussian Federation2021190220212016771Copyright © Бебенина А.А., Чундокова М.А., Смирнов А.Н., Голованёв М.А., Докшукина А.А., 20212021Бебенина А.А., Чундокова М.А., Смирнов А.Н., Голованёв М.А., Докшукина А.А.Bebenina A.A., Chundokova M.A., Smirnov A.N., Golovanev M.A., Dokshukina A.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://vsp.spr-journal.ru/jour/article/view/2562Background

Background. KID syndrome (keratitis-ichthyosis-deafness) is an orphan genetic multisystem disease with autosomal recessive and dominant types of inheritance, it manifests in the neonatal period. The leading triad of symptoms is: skin lesions, ophthalmological diseases and hearing organ pathology. Clinical Case Description. Girl V., 17 years old, with KID syndrome applied to the hospital complaining on painful infiltrates of the parietal region. Multiple abscesses were lanced. Hyperkeratotic crusts were removed, unviable skin regions were excised, and abscesses' cavities were washed with antiseptic solution during daily dressings. Purulent discharge from wounds has been maintaining for 7 days. Conclusion. Where is no pathogenetic treatment for KID syndrome yet. Prevention of secondary surgical infections remains the crucial aspect in the management of such patients. Local wound treatment, symptomatic and antibacterial therapy are effective in case of skin infection.

 

 

KID-синдромвторичная инфекциядетиклинический случайабсцессKID syndromesecondary infectionchildrenclinical caseabscessНе указан.Not specified.ReferencesЛяшенко Н.В., Колясева Н.А. KID-синдром: эритродермия врожденная ихтиозиформная с глухотой и кератитом // Здоровье, демография, экология финно-угорских народов. — 2016. — № 4. — С. 39-41.Lyashenko NV, Kolyaseva NA. KID syndrome: congenital ichthyosiform erythroderma with deafness and keratitis. Health, Demography, Ecology of Finno-Ugric People. 2016;(4):39-41. (In Russ).Маркова Т.Г., Бражкина Н.Б., Близнец Е.В. и др. Диагностика синдрома кератита-ихтиоза-глухоты (КИД-синдром) // Вестник оториноларингологии. — 2012. — № 3. — С. 58-61.Markova TG, Brazhkina NB, Bliznets EA, et al. Diagnostics of keratitis-ichthyosis-deafness syndrome (KID-syndrome). Vestnik otorinolaringologii = Bulletin of Otorhinolaryngology. 2012;(3):58-61. (In Russ).Gonzalez ME, Tlougan BE, Price HN, et al. Keratitis-ichthyosis-deafness (KID) syndrome. Dermatol Online J. 15;(8):11.Gonzalez ME, Tlougan BE, Price HN, et al. Keratitis-ichthyosis-deafness (KID) syndrome. Dermatol Online J. 15;(8):11.Dey VK, Saxena A, Parikh S. KID Syndrome: A Rare Geno-dermatosis. Indian Dermatol Online J. 2020;11(1):116-118. doi: 10.4103/idoj.IDOJ_87_19Dey VK, Saxena A, Parikh S. KID Syndrome: A Rare Geno-dermatosis. Indian Dermatol Online J. 2020;11(1):116-118. doi: 10.4103/idoj.IDOJ_87_19Клименко В.А., Здыбская Е.П., Сиренко Т.В. и др. Клиническое наблюдение ребенка с КИД (кератид-ихтиоз-глухота) синдромом // Здоровье ребенка. — 2015. — Т. 6. — № 66. — С. 129-132.Klymenko VA, Zdybska OP, Sirenko TV, et al. Clinical observation of a child with KID (keratitis-ichthyosis-deafness) syndrome. Child's Health. 2015;6(66):129-132. (In Russ).Abdollahi A, Hallaji, Esmaili N, et al. KID syndrome. Dermatol Online J. 2007;13(4):11.Abdollahi A, Hallaji, Esmaili N, et al. KID syndrome. Dermatol Online J. 2007;13(4):11.Coggshall K, Farsani T, Ruben B, et al. Keratitis, ichthyosis, and deafness (KID) syndrome: a review of infectious and neoplastic complications. J Am Acad Dermatol. 2013;69(1):127-134. doi: 10.1016/j.jaad.2012.12.965Coggshall K, Farsani T, Ruben B, et al. Keratitis, ichthyosis, and deafness (KID) syndrome: a review of infectious and neoplastic complications. J Am Acad Dermatol. 2013;69(1):127-134. doi: 10.1016/j.jaad.2012.12.965Jovanovic D, Paravina M, Stanojevic M, et al. Keratitis, ichthyosis and deafness (KID) syndrome: case study. Acta Med Median. 1998;5:67-72.Jovanovic D, Paravina M, Stanojevic M, et al. Keratitis, ichthyosis and deafness (KID) syndrome: case study. Acta Med Median. 1998;5:67-72.Stepanovic M, Paravina M, Jankovic, Janjic Spasic D. Keratitis, Ichthyosis and Deafness (KID) Syndrome — a Case Report. Serbian J Dermatol Venereol. 2013;5(1):22-30. doi: 10.2478/sjdv-2013-0003Stepanovic M, Paravina M, Jankovic, Janjic Spasic D. Keratitis, Ichthyosis and Deafness (KID) Syndrome — a Case Report. Serbian J Dermatol Venereol. 2013;5(1):22-30. doi: 10.2478/sjdv-2013-0003Alli N, Gungor E. Keratitis, ichthyosis and deafness (KID) syndrome. Int J Dermatol. 1997;36:37-40.Alli N, Gungor E. Keratitis, ichthyosis and deafness (KID) syndrome. Int J Dermatol. 1997;36:37-40.Kapila A, De Baerdemaeker R, Bakal F, et al. A Rare Case of KID Syndrome: The Use of Hydrosurgery and Strategies for Antiseptic Wound Care. Adv Skin Wound Care. 2019;32(10):1-6. doi: 10.1097/01.ASW.0000580480.86585.3aKapila A, De Baerdemaeker R, Bakal F, et al. A Rare Case of KID Syndrome: The Use of Hydrosurgery and Strategies for Antiseptic Wound Care. Adv Skin Wound Care. 2019;32(10):1-6. doi: 10.1097/01.ASW.0000580480.86585.3aМурашкин Н.Н., Амбарчян Э.Т., Епишев Р.В., Материкин А.И. Барьерные свойства кожи в норме и патологии // Педиатрия. Журнал им. Г.М. Сперанского. — 2015. Т. 94. — № 6. — С. 165-169.Murashkin NN, Ambarchyan ET, Epishev RV, Materikin AI. Skin barrier properties in norm and pathology. Pediatria n.a. G.N. Speransky. 2015;94(6):165-169. (In Russ).Гостищев В.К. Общая хирургия: учебник. — 4-е изд., перераб. и доп. — М.: ГЭОТАР-медиа; 2010. — 848 с.Gostishchev V.K. Obshchaya khirurgiya: Textbook. — 4th ed. upd. and rev. Moscow: GEOTAR-media; 2010. 848 p. (In Russ).

The authors declare that there are no conflicts of interest present.