vspВопросы современной педиатрииCurrent Pediatrics1682-55271682-5535Издательство «ПедиатрЪ»10.15690/vsp.v12i5.796vsp-278Research ArticleНЕПРЕРЫВНОЕ ПРОФЕССИОНАЛЬНОЕ ОБРАЗОВАНИЕPROFESSIONAL DEVELOPMENTДИЕТОТЕРАПИЯ ПРИ КЛАССИЧЕСКОЙ ФЕНИЛКЕТОНУРИИ: КРИТЕРИИ ВЫБОРА СПЕЦИАЛИЗИРОВАННЫХ ПРОДУКТОВ БЕЗ ФЕНИЛАЛАНИНАDIETOTHERAPY OF CLASSICAL PHENYLKETONURIA: CRITERIA FOR CHOOSING SPECIALIZED PHENYLALANINE-FREE PRODUCTSБоровикТ. Э.BorovikT. E.

Borovik Tatyana Eduardovna, Doctor of Medical Sciences, Head Professor of the Department of Healthy and Sick Child Nutrition

borovik@nczd.ruЛадодоК. С.LadodoK. S.borovik@nczd.ruБушуеваТ. В.BushuevaT. V.borovik@nczd.ruТимофееваА. Г.TimofeevaA. G.borovik@nczd.ruКоньИ. Я.Kon'I. Ya.borovik@nczd.ruКругликВ. И.KruglikV. I.borovik@nczd.ruВолковаИ. Н.VolkovaI. N.borovik@nczd.ruНаучный центр здоровья детей РАМН, Москва; Первый московский государственный медицинский университет им. И.М. СеченоваРоссияScientific Centre of Children Health, RAMS, Moscow; I.M. Sechenov First Moscow State Medical UniversityRussian FederationНаучный центр здоровья детей РАМН, МоскваРоссияScientific Centre of Children Health, RAMS, MoscowRussian FederationНИИ питания РАМН, МоскваРоссияScientific Research Institute of Nutrition, RAMS, MoscowRussian Federation201319092013125Вопросы современной педиатрии4048Copyright © Боровик Т.Э., Ладодо К.С., Бушуева Т.В., Тимофеева А.Г., Конь И.Я., Круглик В.И., Волкова И.Н., 20132013Боровик Т.Э., Ладодо К.С., Бушуева Т.В., Тимофеева А.Г., Конь И.Я., Круглик В.И., Волкова И.Н.Borovik T.E., Ladodo K.S., Bushueva T.V., Timofeeva A.G., Kon' I.Y., Kruglik V.I., Volkova I.N.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://vsp.spr-journal.ru/jour/article/view/278

В статье обосновываются современные критерии выбора специализированных продуктов на основе L-аминокислот без фенилаланина, предназначенных для лечения больных фенилкетонурией всех возрастных групп.

The article contains evidence-based modern criteria for choosing specialized phenylalanine-free foods with L-amino-acids, designed for phenylketonuria treatment in patients of all age groups.

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The authors declare that there are no conflicts of interest present.