vspВопросы современной педиатрииCurrent Pediatrics1682-55271682-5535Издательство «ПедиатрЪ»10.15690/vsp.v21i5.2460vsp-3038Research ArticleКЛИНИЧЕСКИЕ НАБЛЮДЕНИЯCLINICAL OBSERVATIONSПоражение лица при локализованной склеродермии по типу «удар саблей» в детском возрасте: современное лечение и коррекция последствийFace Lesions in En Coup De Sabre Scleroderma in Children: Modern Treatment and Outcomes Improvementhttps://orcid.org/0000-0003-2252-8570МурашкинН. Н.MurashkinNikolay N.

Мурашкин Николай Николаевич - доктор медицинских наук, заведующий отделением дерматологии с группой лазерной хирургии, заведующий лабораторией патологии кожи у детей отдела научных исследований в педиатрии НМИЦ здоровья детей, профессор кафедры дерматовенерологии и косметологии ЦГМА, профессор кафедры педиатрии и детской ревматологии ФГАОУ ВО Первый МГМУ им. И.М. Сеченова (Сеченовский Университет).

119296, Москва, Ломоносовский пр-т, д. 2, стр. 1, тел.: +7 (499) 134-08-89

Moscow

m_nn2001@mail.ruhttps://orcid.org/0000-0001-6884-5171СавеловаА. А.SavelovaAlena A.

Москва

Moscow

https://orcid.org/0000-0002-2789-2999МисбаховаА. Р.MisbakhovaAlina R.

Москва

Moscow

НМИЦ здоровья детей; Первый МГМУ им. И.М. Сеченова (Сеченовский Университет); ЦГМА Управления делами Президента РФРоссияNational Medical Research Center of Children’s Health; Sechenov First Moscow State Medical University; Central State Medical Academy of Department of Presidential AffairsRussian FederationНМИЦ здоровья детейРоссияNational Medical Research Center of Children’s HealthRussian FederationИнститут пластической хирургии и косметологииРоссияInstitute of Plastic Surgery and CosmetologyRussian Federation202208112022215414418Copyright © Мурашкин Н.Н., Савелова А.А., Мисбахова А.Р., 20222022Мурашкин Н.Н., Савелова А.А., Мисбахова А.Р.Murashkin N.N., Savelova A.A., Misbakhova A.R.This work is licensed under a Creative Commons Attribution 4.0 License.https://vsp.spr-journal.ru/jour/article/view/3038

Локализованная склеродермия (ЛС) — это воспалительное склерозирующее заболевание кожи и подкожных тканей, связанное с их атрофией. Как правило, ЛС является доброкачественным самоограничивающимся заболеванием, хотя хроническая форма болезни носит рецидивирующий характер. Особое внимание уделяется поиску методов лечения ЛС, позволяющих устранить не только иммуноопосредованные механизмы заболевания, но и его последствия, выражающиеся в грубых косметических дефектах лица, которые негативно влияют на гармоничность физического и психоэмоционального развития ребенка. В последнее время изучается эффективность пересадки жира с целью воссоздания объема и повышения качества кожи. В статье представлены результаты такого хирургического вмешательства у пациентки (возраст 15 лет) с линейной формой ЛС.

Localized scleroderma (LS) is an inflammatory sclerosing disease of the skin and subcutaneous tissues associated with its atrophy. Commonly, LS is a benign self-limited disease, although, the chronic form of this disease is recurrent. Particular attention is paid to the research of treatments methods that could eliminate not only immune-mediated mechanisms, but also its outcomes (such as gross cosmetic defects on the face), which negatively affect child’s physical and psycho-emotional development. Recently, fat transplantation efficacy has been studied as it can restore the volume and improve skin quality. This article presents the results of such surgery in a patient (15 years old) with linear form of LS.

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The authors declare that there are no conflicts of interest present.