KID Syndrome Complicated by Multiple Abscesses of the Parietal Region Skin: Clinical Case
Anastasia A. Bebenina,
Madina A. Chundokova,
Alexey N. Smirnov,
Maxim A. Golovanev,
Alina A. Dokshukina https://doi.org/10.15690/vsp.v20i1.2240
Abstract
Background. KID syndrome (keratitis-ichthyosis-deafness) is an orphan genetic multisystem disease with autosomal recessive and dominant types of inheritance, it manifests in the neonatal period. The leading triad of symptoms is: skin lesions, ophthalmological diseases and hearing organ pathology. Clinical Case Description. Girl V., 17 years old, with KID syndrome applied to the hospital complaining on painful infiltrates of the parietal region. Multiple abscesses were lanced. Hyperkeratotic crusts were removed, unviable skin regions were excised, and abscesses' cavities were washed with antiseptic solution during daily dressings. Purulent discharge from wounds has been maintaining for 7 days. Conclusion. Where is no pathogenetic treatment for KID syndrome yet. Prevention of secondary surgical infections remains the crucial aspect in the management of such patients. Local wound treatment, symptomatic and antibacterial therapy are effective in case of skin infection.
Supporting agencies: Not specified.
About the Authors
Anastasia A. Bebenina
Pirogov Russian National Research Medical University
Russian Federation
Moscow.
Disclosure of interest:
Russian Federation
Moscow.
Disclosure of interest:
Not declared.
Madina A. Chundokova
Children’s City Clinical Hospital named after N.F. Filatov
Russian Federation
Moscow.
Disclosure of interest:
Russian Federation
Moscow.
Disclosure of interest:
Not declared.
Alexey N. Smirnov
Children’s City Clinical Hospital named after N.F. Filatov
Russian Federation
Moscow.
Disclosure of interest:
Russian Federation
Moscow.
Disclosure of interest:
Not declared.
Maxim A. Golovanev
Pirogov Russian National Research Medical University
Russian Federation
Moscow.
Disclosure of interest:
Russian Federation
Moscow.
Disclosure of interest:
Not declared.
Alina A. Dokshukina
National Medical Research Center for Obstetrics, Gynecology and Perinatology n.a. Academician V.I. Kulakov
Russian Federation
Moscow.
Disclosure of interest:
Russian Federation
Moscow.
Disclosure of interest:
Not declared.
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Review
For citations:
Bebenina A.A., Chundokova M.A., Smirnov A.N., Golovanev M.A., Dokshukina A.A. KID Syndrome Complicated by Multiple Abscesses of the Parietal Region Skin: Clinical Case. Current Pediatrics. 2021;20(1):67-71. (In Russ.) https://doi.org/10.15690/vsp.v20i1.2240
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