Ювенильная болезнь Бехчета: клиническое наблюдение

Болезнь Бехчета относится к системным васкулитам неизвестной этиологии, характеризуется рецидивирующими эрозивно-язвенными поражениями слизистой оболочки рта и половых органов, вовлечением в патологический процесс суставов, центральной нервной системы, органов желудочно-кишечного тракта. Полисистемность клинических проявлений, относительно редкая встречаемость, особенно в детском возрасте, отсутствие патогномоничных лабораторных признаков определяет трудность верификации заболевания. Диагноз болезни Бехчета особенно сложен в случаях, когда интестинальные симптомы представлены в качестве начального или преобладающего проявления заболевания, и они нередко ошибочно расцениваются как воспалительное заболевание кишечника. К этому следует добавить, что диагностика болезни Бехчета основывается на совокупности классификационных/диагностических признаков, развитие которых может быть растянутым на 5–6 и более лет. В статье представлен случай ювенильной болезни Бехчета, демонстрирующий сложность диагностического поиска. В коротком литературном обзоре обсуждается современный взгляд на проблему диагностики заболевания в педиатрической практике, патогенеза, клинической картины и лечения.

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