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THE PROBLEM OF PERMANENT VASCULAR ACCESS IN PATIENTS WITH CONGENITAL COMBINED COAGULATION DISORDER AND THROMBOHEMORRHAGIC SYNDROME (A CLINICAL CASE)

https://doi.org/10.15690/vsp.v11i4.382

Abstract

Treatment of patients with congenital combined coagulation disorder and thrombohemorrhagic syndrome is associated with a number of difficulties, one of them is need of permanent vascular access in order to provide appropriate pathogenetic therapy. The article contains a clinical case, representing a subject matter of searching for means of providing a permanent vascular access in a child with congenital combined deficiency of vitamin K dependent clotting factors (II, VII, IX, X, S- and C-protieins) and severe course of thrombohemorrhagic syndrome.

About the Authors

I. N. Nurmeev
Children Republican Clinical Hospital, Kazan; Kazan State Medical University
Russian Federation
Il’dar Nurmeyev, Doctor of Medical Science, assistant of chair of pediatric surgery of the Kazan State Medical University


L. F. Rashitov
Children Republican Clinical Hospital, Kazan
Russian Federation


References

1. Дементьева И. И., Чарная М. А., Морозов Ю. А. Патология системы гемостаза. М.: ГЭОТАР-Медиа. 2011. 283 с.

2. URL: http://omim.org/entry/277450

3. URL: http://omim.org/entry/607473

4. Brenner B., Tavori S., Zivelin A. et al. Hereditary deficiency of all vitamin K-dependent procoagulants and anticoagulants. Brit. J. Haemat. 1990; 75: 537–542.

5. Oldenburg J., von Brederlow B., Fregin A. et al. Congenital deficiency of vitamin K dependent coagulation factors in two families presents as a genetic defect of the vitamin K-epoxide-reductasecomplex. Thromb. Haemost. 2000; 84: 937–941.

6. Гематология: Новейший справочник / под общ. ред. К. М. Абдулкадырова. М.: Изд-во «Эксмо»; С.-Пб.: Изд-во «Сова». 2004. 928 с., илл.


Review

For citations:


Nurmeev I.N., Rashitov L.F. THE PROBLEM OF PERMANENT VASCULAR ACCESS IN PATIENTS WITH CONGENITAL COMBINED COAGULATION DISORDER AND THROMBOHEMORRHAGIC SYNDROME (A CLINICAL CASE). Current Pediatrics. 2012;11(4):193-195. (In Russ.) https://doi.org/10.15690/vsp.v11i4.382

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ISSN 1682-5527 (Print)
ISSN 1682-5535 (Online)